Successful treatment of refractory hughes stovin syndrome with infliximab

نویسندگان

  • Giulia Gortani
  • Meta Starc
  • Martina Tubaro
چکیده

Introduction Hughes-Stovin Syndrome (HSS) is a very rare clinical disorder characterized by pulmonary artery aneurysms and peripheral venous thrombosis. Typical symptoms are recurrent fever, chills, haemoptysis and it usually affects young men. The natural course of the illness is usually fatal because of fulminant haemoptysis. The aetiology of Hughes-Stovin syndrome is still unknown; however it is supposed to be a clinical variant manifestation of Behçet disease.

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Hughes-Stovin syndrome revealing the presence of Behçet’s Disease

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عنوان ژورنال:

دوره 12  شماره 

صفحات  -

تاریخ انتشار 2014